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Mouse Monoclonal Antibody to ALDH6A1
Black line: Control Antigen (100 ng);Purple line: Antigen (10ng); Blue line: Antigen (50 ng); Red line:Antigen (100 ng)
Mouse Monoclonal Antibody to ALDH6A1
Western blot analysis using ALDH6A1 mouse mAb against Jurkat (1), HEK293 (2), Hela (3), MCF-7 (4), and LNcap (5) cell lysate.
Mouse Monoclonal Antibody to ALDH6A1
Immunofluorescence analysis of Hela cells using ALDH6A1 mouse mAb. Blue: DRAQ5 fluorescent DNA dye. Red: Actin filaments have been labeled with Alexa Fluor- 555 phalloidin.
Mouse Monoclonal Antibody to ALDH6A1
Immunofluorescence analysis of Hela cells using ALDH6A1 mouse mAb (green). Blue: DRAQ5 fluorescent DNA dye. Red: Actin filaments have been labeled with Alexa Fluor- 555 phalloidin. Secondary antibody from Fisher (Cat#: 35503)
Mouse Monoclonal Antibody to ALDH6A1
Flow cytometric analysis of Hela cells using ALDH6A1 mouse mAb (green) and negative control (red).
Mouse Monoclonal Antibody to ALDH6A1
Immunohistochemical analysis of paraffin-embedded human rectum cancer tissues using ALDH6A1 mouse mAb with DAB staining.
Mouse Monoclonal Antibody to ALDH6A1
Immunohistochemical analysis of paraffin-embedded human endometrial cancer tissues using ALDH6A1 mouse mAb with DAB staining.
Mouse Monoclonal Antibody to ALDH6A1
Mouse Monoclonal Antibody to ALDH6A1
Mouse Monoclonal Antibody to ALDH6A1
Mouse Monoclonal Antibody to ALDH6A1
Mouse Monoclonal Antibody to ALDH6A1
Mouse Monoclonal Antibody to ALDH6A1
Mouse Monoclonal Antibody to ALDH6A1

Mouse Monoclonal Antibody to ALDH6A1

  • 货号:

    30974
  • 别名:

    MMSDH; MMSADHA
  • 产品上架时间:

    2024-01-01
  • 应用:

    WB,IHC,IF,FCM
  • 反应种属:

    Human
  • 抗体类型:

    Primary antibody
  • Swissprot:

    Q02252
  • 规格:

  • 数量:

    -
    +
  • 说明书:

    目录价¥2180

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Mouse Monoclonal Antibody to ALDH6A1

Description

This gene encodes a member of the aldehyde dehydrogenase protein family. The encoded protein is a mitochondrial methylmalonate semialdehyde dehydrogenase that plays a role in the valine and pyrimidine catabolic pathways. This protein catalyzes the irreversible oxidative decarboxylation of malonate and methylmalonate semialdehydes to acetyl- and propionyl-CoA. Methylmalonate semialdehyde dehydrogenase deficiency is characterized by elevated beta-alanine, 3-hydroxypropionic acid, and both isomers of 3-amino and 3-hydroxyisobutyric acids in urine organic acids. Alternate splicing results in multiple transcript variants.

References

1.Orphanet J Rare Dis. 2013 Jul 9;8:98.
2.J Inherit Metab Dis. 2012 May;35(3):437-42.

Specification

Aliases MMSDH; MMSADHA
Entrez GeneID 4329
Swissprot Q02252
clone 6H9B8
WB Predicted band size 57.8kDa
Host/Isotype Mouse IgG1
Antibody Type Primary antibody
Storage Store at 4°C short term. Aliquot and store at -20°C long term. Avoid freeze/thaw cycles.
Species Reactivity Human
Immunogen Purified recombinant fragment of human ALDH6A1 (AA: 1-195) expressed in E. Coli.
Formulation Purified antibody in PBS with 0.05% sodium azide

Application

WB 1/500 - 1/2000
IHC 1/200 - 1/1000
IF/ICC 1/200 - 1/1000
FCM 1/200 - 1/400
ELISA 1/10000