Rabbit Monoclonal Antibody to Galactosidase alpha

Description
Defects in GLA are the cause of Fabry disease (FD) [MIM:301500]. FD is a rare X-linked sphingolipidosis disease where glycolipid accumulates in many tissues. The disease consists of an inborn error of glycosphingolipid catabolism.

Specification
Aliases	Alpha gal A; GALA; Galactosidase; alpha; GLA; Melibiase
Entrez GeneID	2717
Swissprot	P06280
WB Predicted band size	Calculated MW: 49 kDa; Observed MW: 49 kDa
Host/Isotype	Rabbit IgG
Antibody Type	Primary antibody
Storage	Store at 4°C short term. Aliquot and store at -20°C long term. Avoid freeze/thaw cycles.
Species Reactivity	Human
Immunogen	A synthetic peptide of human Galactosidase alpha
Formulation	Purified antibody in TBS with 0.05% sodium azide,0.05%BSA and 50% glycerol.

Application
WB	1/500-1/1000
IP	1/10-1/20
IHC	1/50-1/100